,,iii #aai? ,,congress #a/ ,session ,s4 ,,res4 #dii ,,9 ,,! ,,s5ate ,,( ,,! ,,unit$ ,,/ates ,novemb] #ah1 #bjbe ,mr4 ,hu/$ submitt$ ! foll[+ resolution2 :i* 0 ref]r$ to ! ,committee on ,heal?1 ,education1 ,labor1 & ,p5sions ,,resolution ,support+ ! goals & ideals ( ,creutzfeldt-,jakob ,disease 7,,cjd7 ,aw>5ess ,day4 ,:]eas ,creutzfeldt-,jakob disease 7,,cjd7 is a r>e1 fatal bra9 disord] )9 a gr\p ( illnesses call$ prion diseases2 ,:]eas ,,cjd occurs 9 approximately #a to #b individuals p] #a1jjj1jjj ea* ye>1 result+ 9 approximately #fjj cases annually 9 ! ,unit$ ,/ates1 #he p]c5t ( :i* are designat$ z sporadic1 ) no kn[n causes1 :ile #aj to #ae p]c5t are deem$ g5etic1 & less ?an #a p]c5t are deem$ acquir$2 ,:]eas1 9 ! e>ly /ages ( ! disease1 ,,cjd pati5ts may exhibit fail+ memory1 behavioral *anges1 impair$ coord9ation1 & visual di/urbances1 & z ! illness progresses m5tal det]ioration becomes m pron\nc$ :ile involunt>y movem5ts1 bl9dness1 weakness ( extremities1 & ultimately coma may occur2 ,:]eas ,,cjd typically leads to dea? )9 a few mon?s to #a ye> foll[+ ! onset ( symptoms2 ,:]eas ,,cjd is responsible = #a 9 e #f1jjj dea?s 9 ! ,unit$ ,/ates ea* ye>2 ,:]eas compreh5sive prion disease surveillance is critical 9 ord] to develop m effici5t detection me?ods & to det]m9e :e!r humans c acquire ! disease ?r\gh ! consumption ( prion-contam9at$ beef 7kn[n to cause bov9e spongi=m encephalopa?y 7,,bse7 or mad c[ disease7 or meat f c]vids 7de]1 elk1 & moose7 affect$ by *ronic wa/+ disease 7ref]r$ to 9 ?is preamble z ,,cwd72 ,:]eas ,,cwd is a fatal condition 9 c]vids1 caus$ by misfold$ prions1 t has be5 detect$ 9 c]vids 9 m ?an #cf ,/ates & all #d regions ( ! ,unit$ ,/ates2 ,:]eas monitor+ ! preval5ce ( prion diseases1 includ+ det]m9+ a disease's incid5ce & :e!r x 0 acquir$ f animals or o!r humans1 is critical2 ,:]eas cont9u$ prion disease surveillance1 p>ticul>ly ?r\gh exam9ation ( po/mortem human bra9 tissue1 is imp]ative to evaluate :e!r ,,cwd has or c spread to humans2 ,:]eas ! ,national ,prion ,disease ,pa?ology ,surveillance ,c5t] is ! only laboratory-bas$ organization 9 ! ,unit$ ,/ates t monitors human prion diseases1 :i* is critical to protect+ ! public heal? ( ! ,unit$ ,/ates2 ,:]eas ,alzheim]'s disease & relat$ dem5tias 7ref]r$ to 9 ?is preamble z ,,adrd7 rese>* c\ld b5efit f ! /udy ( prion diseases1 l ,,cjd2 ,:]eas c>egiv] & heal?-s]vices rese>* ( ,,adrd %\ld be appli$ to prion diseases1 l ,,cjd1 :i* %>e _m ( ! same *all5ges2 ,:]eas ! families & communities affect$ by ,,cjd h compell+ /ories due to ! r>ity & rapid effects ( ! disease2 ,:]eas1 f ! "t ( diagnosis1 ,,cjd pres5ts unique *all5ges & burd5s = pati5ts1 _! family memb]s1 & c>egiv]s giv5 ! rapidly progressive nature ( ?is deva/at+ disease2 & ,:]eas ! e/abli%m5t ( ,novemb] #ab1 #bjbe1 z ,creutzfeldt-,jakob ,disease 7,,cjd7 ,aw>5ess ,day w\ld raise aw>5ess ab\t ?is r>e1 rapidly progressive1 & inv>iably fatal disease3 ,n[1 !re=e1 be x ,t ! ,s5ate-- 7#a7 supports ! goals & ideals ( ,creutzfeldt-,jakob ,disease 7,,cjd7 ,aw>5ess ,day2 & 7#b7 recognizes ! importance ( rais+ aw>5ess ( ?is r>e bra9 disord]4