,,iv #aah? ,,congress #a/ ,session ,h4 ,,res4 #hba ,,9 ,,! ,,h\se ,,( ,,repres5tatives ,octob] #bf1 #bjbc,mr4 ,valadao 7= himself1 ,mr4 ,co/a1 ,ms4 ,br[n1 ,ms4 ,slotk91 ,mr4 ,joyce ( ,ohio1 & ,mr4 ,mc,carthy7 submitt$ ! foll[+ resolution2 :i* 0 ref]r$ to ! ,committee on ,en]gy & ,comm]ce ,,resolution ,support+ ! goals & ideals ( ,creutzfeldt-,jakob ,disease 7,,cjd7 ,aw>5ess ,day4 ,:]eas ,creutzfeldt-,jakob ,disease 7ref]r$ to 9 ?is resolution z ,,cjd7 is a r>e1 fatal bra9 disord] )9 a gr\p ( illnesses call$ prion diseases2 ,:]eas ,,cjd occurs 9 approximately #a to #b cases p] million individuals ea* ye>1 result+ 9 approximately #ejj cases annually 9 ! ,unit$ ,/ates1 #he p]c5t ( :i* are designat$ z sporadic1 ) no kn[n causes1 :ile #aj to #ae p]c5t are deem$ g5etic & few] ?an #a p]c5t are deem$ acquir$2 ,:]eas1 9 ! e>ly /ages ( ! disease1 ,,cjd pati5ts may exhibit fail+ memory1 behavioral *anges1 impair$ coord9ation1 & visual di/urbances1 & z ! illness progresses1 & m5tal det]ioration becomes m pron\nc$ :ile involunt>y movem5ts1 bl9dness1 weakness ( extremities1 & ultimately coma may occur2 ,:]eas ,,cjd typically leads to dea? )9 a few mon?s to #a ye> foll[+ ! onset ( symptoms2 ,:]eas compreh5sive prion disease surveillance is critical 9 ord] to develop m effici5t detection me?ods1 & to det]m9e :e!r humans c acquire ! disease ?r\gh ! consumption ( prion contam9at$ beef 7kn[n to cause ,bov9e ,spongi=m ,encephalopa?y 7,,bse7 or mad c[ disease7 or meat f elk & de] affect$ by ,*ronic ,wa/+ ,disease 7,,cwd72 ,:]eas cont9u$ prion disease surveillance1 p>ticul>ly ?r\gh exam9ation ( po/mortem human bra9 tissue1 is imp]ative to evaluate :e!r ,,cwd has or c spread to humans2 ,:]eas ,alzheim]'s ,disease & ,relat$ ,dem5tias 7,,adrd7 rese>* c\ld b5efit f ! /udy ( prion diseases1 l ,,cjd2 ,:]eas c>egiv] & heal? s]vices rese>* ( ,,adrd %\ld be appli$ to prion diseases1 l ,,cjd1 :i* %>es _m ( ! same *all5ges2 ,:]eas ! families & communities affect$ by ,,cjd h a compell+ /ory due to ! r>ity & rapid effects ( ! disease2 ,:]eas f ! "t ( diagnosis ,,cjd pres5ts unique *all5ges & burd5s = pati5ts1 _! family memb]s & c>egiv]s giv5 ! rapidly progressive nature ( ?is deva/at+ disease2 & ,:]eas ! e/abli%m5t ( ,novemb] #ab1 #bjbc1 z ,creutzfeldt-,jakob ,disease 7,,cjd7 ,aw>5ess ,day w\ld raise aw>5ess ab\t ?is r>e1 rapidly progressive1 & inv>iably fatal disease3 ,n[1 !re=e1 be x ,t ! ,h\se ( ,repres5tatives-- 7#a7 supports ! goals & ideals ( ,creutzfeldt-,jakob ,disease 7,,cjd7 ,aw>5ess ,day2 & 7#b7 recognizes ! importance ( rais+ aw>5ess ( ?is r>e bra9 disord]4